Intra-cerebral hemorrhage associated with choledochal cyst in an infant

Choledochal cysts usually present with classical triad of jaundice, abdominal pain and palpable mass in infants. Presentation with gastrointestinal bleeding secondary to obstructive jaundice has been described in literature but with intracranial bleeding is exceedingly rare. Herein we describe a case who presented with seizures and signs of intra cranial hemorrhage [ICH]. On evaluation he was found to have huge choledochal cyst and marked jaundice. He was initially managed for ICH and subsequently underwent cyst excision with Roux-en-Y hepaticojejunostomy. Post op recovery was uneventful with mild neurological deficit.