TY - JOUR
T1 - Systemic Artery Aneurysm in Two Children with Kawasaki Disease
T2 - A Frequently Overlooked Lesion
AU - Ahmed, Shaikh Habiba
AU - Ahmed, Shakeel
AU - Farooq, Shafiq Ur Rehman
AU - Akhtar, Saleem
N1 - Publisher Copyright:
© 2025 College of Physicians and Surgeons Pakistan. All rights reserved.
PY - 2025/1
Y1 - 2025/1
N2 - Kawasaki disease (KD) is a multisystem vasculitis affecting medium-sized arteries. While coronary involvement is a well-documented complication, extensive disease is often associated with systemic arterial involvement. Multiple studies have reported the occurrence of systemic and pulmonary arterial involvement. This atypical presentation underscores the importance of a thorough diagnostic evaluation, including early echocardiography, radiological imaging, and CT angiography, when KD is suspected. Early identification of atypical presentations can significantly improve the disease prognosis by reducing the risks of vascular stenosis, obstruction, and thrombosis. This case series highlights the underexplored atypical presentations of KD, emphasising the necessity for timely recognition, investigation, and management of systemic and pulmonary arterial involvement alongside coronary complications.
AB - Kawasaki disease (KD) is a multisystem vasculitis affecting medium-sized arteries. While coronary involvement is a well-documented complication, extensive disease is often associated with systemic arterial involvement. Multiple studies have reported the occurrence of systemic and pulmonary arterial involvement. This atypical presentation underscores the importance of a thorough diagnostic evaluation, including early echocardiography, radiological imaging, and CT angiography, when KD is suspected. Early identification of atypical presentations can significantly improve the disease prognosis by reducing the risks of vascular stenosis, obstruction, and thrombosis. This case series highlights the underexplored atypical presentations of KD, emphasising the necessity for timely recognition, investigation, and management of systemic and pulmonary arterial involvement alongside coronary complications.
KW - Atypical Kawasaki disease
KW - Giant coronary artery aneurysm
KW - Systemic artery aneurysm
UR - https://www.scopus.com/pages/publications/105017989091
U2 - 10.29271/jcpspcr.2025.398
DO - 10.29271/jcpspcr.2025.398
M3 - Article
AN - SCOPUS:105017989091
SN - 1022-386X
VL - 35
SP - 398
EP - 401
JO - Journal of the College of Physicians and Surgeons--Pakistan : JCPSP
JF - Journal of the College of Physicians and Surgeons--Pakistan : JCPSP
IS - 1
ER -